Reinard, Thomas; Janke, Viktoria; Willard, Jan; Buck, Fritz; Jacobsen, Hans-Jörg; Vockley, Jerry
(Bethesda, Md. : ASBMB Publications, 2000)
Isovaleryl-CoA dehydrogenase (IVD, EC 1.3.99.10) catalyzes the third step in the catabolism of leucine in mammals. Deficiency of this enzyme leads to the clinical disorder isovaleric acidemia. IVD has been purified and ...